Hirayama's disease

Author: mmuc

August undefined, 2024

Web1 set 2024 · The typical MRI findings in Hirayama disease are reported in Table 1 and include loss of normal cervical lordosis, focal cord atrophy and flattening, anterior displacement of the posterior dural sac during cervical flexion, and prominence of the posterior epidural venous plexus. 1, 21, 31, 35 The exact underlying pathophysiology … Web1 feb 2024 · Hirayama disease (HD), which is also referred to as juvenile muscular atrophy of the distal upper extremities or monomelic amyotrophy, is a special …

Hirayama disease: MRI spectrum of a rare disease Eurorad

Web15. Kano M (1998) Electrophysiology of Hirayama disease. Neurol Med 48: 324-328. 16. Song J, Wang HL, Zheng CJ, Jiang JY (2024) Risk factors for surgical results of Hirayama disease: A retrospective analysis of a large cohort. World Neurosurg 105: 69-77. 17. Wang HL, Wu YW, Song J, Jiang JY, Lu FZ, et al. (2024) Cortical activation changes in ... Web20 feb 2024 · Hirayama is a rare nonfamiliar monomelic amyotrophy also known as benign juvenile brachial spinal muscular atrophy, juvenile asymmetric segmental spinal muscular atrophy, juvenile muscular atrophy of the distal upper extremity, monomelic amyotrophy, and oblique amyotrophy. temperature bd

Hirayama Disease: A Rare Disease with Unusual Features

WebAbstract. Purpose: Hirayama disease is an initially progressive disease caused by cervical neck flexion compressing the anterior horns of the lower cervical spinal cord. It is primarily seen in young males of Indian or Asian descent. With increasing dispersion of these populations this condition is increasingly being encountered internationally. Web21 ago 2024 · Magnetic resonance imaging (MRI) features are typical findings in Hirayama disease (HD) and are useful diagnostic entities but may not be present in all patients. We present the case of a 22-year-old Nepalese man who presented with insidious onset of weakness of his right upper limb of more than 5 years duration. His weakness was … Web29 ago 2024 · Hirayama disease (HD) was first described in 1959; 1 however, further elucidation of its pathophysiology was not fully understood until 1987, resulting in its eponym, Hirayama disease. 2 Cervical myelopathy, caused by repetitive flexion of the neck resulting in forward displacement of the posterior dural sack with compression and injury … temperature batz sur mer

Electric shocks and weakness of the right hand in a young man: Hirayama …

Hirayama Disease - StatPearls - NCBI Bookshelf

Hirayama disease, also termed non-progressive juvenile spinal muscular atrophy of the distal upper limbs, is a type of cervical myelopathy related to flexion movements of the neck. It is considered a benign motor neuron disorder with a stationary stage after a progressive course 1,7 . Visualizza altro It is often of insidious onset presenting with a predominantly unilateral upper extremity weakness and atrophy, cold paresis, and no … Visualizza altro Chronic microcirculatory changes in the territory of the anterior spinal artery induced by repeated or sustained flexion account for the necrosis of the anterior horns … Visualizza altro Management options include long-term cervical soft braces, which is the first-line management, or surgical options 7. Regardless of the management strategy, the disease usually arrests after 3-5 years 7. Visualizza altro On myelograms and flexion-extension MR images, there can be a forward migration of the posterior wall of the dura mater. The posterior … Visualizza altro WebHirayama’s Disease primarily affects young males in countries like India, Sri Lanka, Japan, Taiwan, and Singapore, although there have been cases in non-Asian countries too. The … temperature bebe 34 4Web21 lug 2016 · Hirayama disease is a slowly progressing benign motor neuron disease that affects the distal upper limb. A 29-year-old man visited the hospital with a 1-year history of weakened left proximal upper limb. He was diagnosed with Hirayama disease 9 years ago, while there was no further progression of the muscle weakness afterward. temperature bebe 35 2

"WebThe authors report the case of a 16-year-old boy with Hirayama's disease(juvenile muscular atrophy of unilateral upper extremity). The present history began about 6 months … " - Hirayama's disease

Hirayama disease: MRI spectrum of a rare disease Eurorad

Hirayama Disease: A Rare Disease with Unusual Features

Hirayama's disease

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